Reviewing recherche presentations of persistent Mullerian duct syndrome: case reports

نویسندگان

چکیده

Abstract Background Persistent Mullerian Duct Syndrome (PMDS) is a type of pseudo-hermaphroditism occurring in males internally due to failure the Anti Hormone (AMH)-dependent sex differentiation pathway. Due absent (AMH), adult male has both Wolffian and duct derivatives. Considering limited information available existing literature, malignant transformation PMDS rarely been reported. Case Presentation In this article we present two cases which have complicated malignancy with review literature histopathological correlation. Both these patients presented lower abdominal pain, for computed tomography abdomen pelvis was performed following ultrasound derivates were visualized on above mentioned scans genetically confirmed (46 XY). Conclusion Familiarity necessary diagnose condition. Hence, article, report recherche presentations had into malignancies.

برای دانلود رایگان متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

گزارش یک مورد نادر بیماری مادرزادی: Persistent Mullerian Duct Syndrome (PMDS) در یک آقای 71 ساله

Persistent Mullerian Duct Syndrome in a 71-Year-Old Man, Case Report H. Salehi MD , M.R. Vatani Baf MD Received:27/06/06 Sent for Revision: 11/10/06 Received Revised Manuscript: 07/02/07 Accepted: 12/02/07 Background and Objective: Normal sexual differentiation occurs in the 6th embryonic week and in a normal embryonic life. Both wolffian and mullerian ducts are present until the onse...

متن کامل

Persistent mullerian duct syndrome with an irreducible inguinal hernia.

Received January 2008 Accepted October 2008 INTRODUCTION Persistent mullerian duct syndrome (PMDS), or hernia uteri inguinale, describes a group of patients with a 46,XY karyotype and normal male external genitalia, but internal mullerian duct structures. Typically, these phenotypic males have unilateral or bilateral undescended testes, bilateral fallopian tubes, a uterus, and an upper vaginal ...

متن کامل

Persistent mullerian duct syndrome associated with transverse testicular ectopia.

Persistent Mullerian Duct Syndrome (PMDS) associated with transverse testicular ectopia (TTE) is rare. Ten cases have been reported in the past. Accurate diagnosis with karyotype and histological analysis is crucial. Surgical management should be geared toward preservation of fertility when possible.

متن کامل

An interesting case of Persistent Mullerian Duct Syndrome- An incidental finding

Persistent Mullerian Duct Syndrome is a rare autosomal recessive disease characterized by persistent Mullerian derivative in patients with 46 XY Karyotype and normal virilization .Here we are presenting a case of incidental finding of Persistent Mullerian Duct Remnants in a 58 yr old man during routine hernioplasty.Histological diagnosis was confirmed by Immunohistochemistry

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

ژورنال

عنوان ژورنال: Egyptian Journal of Radiology and Nuclear Medicine

سال: 2022

ISSN: ['2090-4762', '0378-603X']

DOI: https://doi.org/10.1186/s43055-022-00752-w